"a research on hirschsprung’s disease in amirkabir and bahrami children hospitals "

hirchsprung’s disease is a developmental disorder of the enteric nervous system, characterized by abdsence of ganglion cell in the myenterric and submucosal plexuese along a variable portion of the distal intestine.the purpose of this study is the presentation of a new procedure for reduction of the postoperative complications of hirschsprung’s disease (hd) by offering a modified swenson’s technique. this was a chieved through a 10 years study of 157 patients with hd, of whom 74% were male and 26% wre female. in 100 cases the disease was diagnosed in the early neonatal period, in 129 cases the involved segments were rectosigmoid or shortsegment. our choice of operation was a new modification of swenson’s type of pull through (swenson’s operation + posterior rectal wall myectomy). phatholgical examination has confirmed the diagnosis of hd in all patients. the overall results of surgery were good in 81% and there was no mortality.